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  Indian J Med Microbiol
 

Figure 1: Typical posture (BOS posture) with shoulders externally rotated and adducted, wrists flexed in ulnar deviation, and ulnar deviation of the metacarpophalangeal joints. Additionally, there is truncal hypotonia with hypertonia of the extremities. Also note the generalised hypertrichosis, microcephaly, trigonocephaly, widely set eyes (hypertelorism), flat and wide nasal bridge and small mouth

Figure 1: Typical posture (BOS posture) with shoulders externally rotated and adducted, wrists flexed in ulnar deviation, and ulnar deviation of the metacarpophalangeal joints. Additionally, there is truncal hypotonia with hypertonia of the extremities. Also note the generalised hypertrichosis, microcephaly, trigonocephaly, widely set eyes (hypertelorism), flat and wide nasal bridge and small mouth