Home Print this page Email this page Small font size Default font size Increase font size
Users Online: 257
Home About us Editorial board Search Ahead of print Current issue Archives Submit article Instructions Subscribe Contacts Login 
CASE REPORT
Year : 2021  |  Volume : 10  |  Issue : 8  |  Page : 3154-3158

Budd-Chiari syndrome in small hepatic veins: A diagnostic and therapeutic challenge in a low resource setting


1 General Surgery, University Hospitals Birmingham NHS Trust, Birmingham, UK
2 Department of Primary Care and Mental Health, University of Liverpool, Liverpool, UK
3 Maternal and Child Health Division, International Centre for Diarrheal Diseases Research, Bangladesh, Dhaka, Bangladesh
4 College of Science, Health and Engineering, Austin Health Clinical School of Nursing, La Trobe University, Melbourne, Victoria, Australia
5 General Medicine, Tairunnessa Memorial Medical College and Hospital, Gazipur, Bangladesh
6 General Surgery, Bangabandhu Sheikh Mujib Medical University, Shahbagh, Dhaka, Bangladesh
7 Internal Medicine, Diabetic Association Medical College, Faridpur, Bangladesh

Correspondence Address:
Dr. Emiko Sultana
31 Humphrey Middlemore Drive, Harborne, Birmingham, B17 0JJ, England; Name of Department and Institution: Department of General Surgery, University Hospitals Birmingham NHS Trust, Birmingham
UK
Login to access the Email id

Source of Support: None, Conflict of Interest: None


DOI: 10.4103/jfmpc.jfmpc_2213_20

Rights and Permissions

Introduction: Budd-Chiari syndrome (BCS) is a rare condition affecting one in a million adults. BCS involves outflow obstruction in the hepatic venous system, which can occur anywhere between the small hepatic veins and the atrio-caval junction and cannot be due to heart, pericardial, or hepatic veno-occlusive disease. Case Presentation: We report an exceedingly rare form of BCS with less common initial clinical features in a young poor adult male patient which ignited a diagnostic uncertainty and a therapeutic challenge. The presence of the classical triad of BCS in the absence of major hepatic vein obstruction prompted the medical team to consider that the patient had a rare form of BCS. In this case, the financial condition of the patient and limited resources available restricted our ability to advance into the specific investigations. However, the patient was given symptomatic medical treatment and was followed up monthly. We also provided the patient with a statement that reaffirmed our inability to provide affordable surgical management options and called for an optimized national clinical guideline that could help the physicians deal with the challenges. Conclusion: An uncommon form of BCS in this patient provided a diagnostic challenge and therapeutic uncertainty in the low-resource settings. Primary care physicians should commence evidenced medical management based on clinical suspicion acknowledging the fact that obstruction of small hepatic veins is often not detected on an ultrasound.


[FULL TEXT] [PDF]*
Print this article     Email this article
 Next article
 Previous article
 Table of Contents

 Similar in PUBMED
 Related articles
 Citation Manager
 Access Statistics
 Reader Comments
 Email Alert *
 Add to My List *
 * Requires registration (Free)
 

 Article Access Statistics
    Viewed674    
    Printed0    
    Emailed0    
    PDF Downloaded38    
    Comments [Add]    

Recommend this journal